A Case of Multiple Rhabdomyosarcomas of the Small Intestine.

Accession number;03A0117085
Title;A Case of Multiple Rhabdomyosarcomas of the Small Intestine.
Author; YOSHIMURA ATSUSHI (Kokuho Central Hospital, JPN) KANAMURA TETSUHIRO (Kokuho Central Hospital, JPN) SHIBAJI TAKAMUNE (Kokuho Central Hospital, JPN) YOSHIKAWA TAKASHI (Kokuho Central Hospital, JPN)
Journal Title;Journal of Japan Surgical Association
Journal Code:Z0103A
ISSN:1345-2843
VOL.64;NO.1;PAGE.131-136(2003)
Figure&Table&Reference;FIG.4, TBL.3, REF.11
Pub. Country;Japan
Language;Japanese
Abstract;A 33-year-old man was admitted to the hospital because of abdominal pain. Due to the intensifying abdominal pain, an emergency operation was performed on the 6th hospital day. Upon laparotomy, six tumors were present in the small intestine, five of the six tumors were from egg- to fist-sized to cause intestinal obstruction, and the intestine involving the tumors severely dilated. Although a partial resection of the small intestine was performed, remnant tumors at the operative wound, liver and lymph nodes grew extraordinarily rapidly and the patient expired on the 44th post operative day. Pathological examination showed undifferentiated spindle cells and round cells with vascular invasion and tumor necrosis. Immunostaining showed positive reaction to myoglobin and desmine. Subsequently, rhabdomyosarcoma was diagnosed. Rhabdomyosarcoma is common in the soft tissues of the head and neck or genito-urinary tract, but is very rare in the gastrointestinal tract, either primary or matastatic. In this patient who had multiple intestinal tumors and followed a very poor clinical course, these tumors are inferred to be metastasis from unknown primary lesion, though its etiology is obscure. (author abst.)