Diagnosis and Management of Cantrell's Pentalogy
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Accession number;05A0160472
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| Title;Diagnosis and Management of Cantrell's Pentalogy |
| Author;
IKEDA TARO
(Nihon Univ., Sch. of Med.)
KOSHINAGA TSUGUMICHI
(Nihon Univ., Sch. of Med.)
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Journal Title;Japanese Journal of Pediatric Surgery
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Journal Code:Z0323B
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ISSN:0385-6313
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VOL.37;NO.1;PAGE.50-52(2005)
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| Figure&Table&Reference;FIG.1, TBL.1, REF.12 |
| Pub. Country;Japan |
| Language;Japanese |
| Abstract;Cantrell, Haller, and Ravitch in 1958 described a syndrome with five anomalies, since called Cantrell's pentalogy, consisting of a defect of the lower sternum, midline supraumbilical abdominal wall defect, deficiency of the anterior diaphragm, defect in the diaphragmatic pericardium, and congenital intracardiac defect. Most cases are sporadic. Survival rate of patients with complete pentalogy of Cantrell is very low, and the outcome depends on the cardiac malformation. Diagnosis is comparatively easy and most often can be carried out prenatally. Surgical medical treatments are varied. However, because this disease has a poor prognosis, it is important that intensive prenatal management in collaboration with neonatal treatment be implemented. (author abst.) |
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