Diagnosis and Treatment of Body Stalk Anomaly
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Accession number;05A0160480
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| Title;Diagnosis and Treatment of Body Stalk Anomaly |
| Author;
KANAMORI YUTAKA
(Univ. of Tokyo)
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Journal Title;Japanese Journal of Pediatric Surgery
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Journal Code:Z0323B
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ISSN:0385-6313
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VOL.37;NO.1;PAGE.91-96(2005)
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| Figure&Table&Reference;FIG.2, TBL.1, REF.11 |
| Pub. Country;Japan |
| Language;Japanese |
| Abstract;The term "body stalk anomaly" refers to a complicated syndrome that is manifested by giant omphalocele, prominent scoliosis, abnormal development of umbilical cord, and some other anomalies including facial and cranial abnormalities, cardiac diseases, limb deficiency, etc. The exact cause of the disease is not yet apparent, but it might be caused by the abnormal development of the fetus in the very early phase, i.e., 4 to 6 weeks of gestation. The prognosis of the disease is very poor, and only four cases have survived so far. We report a new case of body stalk anomaly; the patient has survived for two years since birth. She now has a tracheostomy and an enterostomy (the latter was accidentally formed in the course of conservative closing of omphalocele by skin tissue elongation). Body stalk anomaly is a very difficult syndrome to treat, but it is anticipated that more patients will survive in the future with the advances in treating severe respiratory failure. (author abst.) |
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