Beckwith-Wiedemann Syndrome
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Accession number;05A0160481
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| Title;Beckwith-Wiedemann Syndrome |
| Author;
TAHARA HIROYUKI
(Kagoshima Univ., JPN)
TAKAMATSU HIDEO
(Kagoshima Univ., JPN)
KAJI TATSURU
(Kagoshima Univ., JPN)
IKEE TAKAMASA
(Kagoshima Univ., JPN)
HAYASHIDA YOSHIHIRO
(Kagoshima Univ., JPN)
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Journal Title;Japanese Journal of Pediatric Surgery
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Journal Code:Z0323B
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ISSN:0385-6313
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VOL.37;NO.1;PAGE.97-101(2005)
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| Figure&Table&Reference;FIG.3, TBL.3, REF.15 |
| Pub. Country;Japan |
| Language;Japanese |
| Abstract;Children with Beckwith-Wiedemann syndrome (BWS), a congenital overgrowth syndrome characterized by exomphalos, macroglossia, and gigantism, have an increased risk of developing childhood tumors including Wilms tumor, hepatoblastoma, neuroblastoma, and rhabdomyosarcoma. We present a case of mediastinal neuroblastoma and a case of metachronous bilateral virilizing adrenocortical tumors with BWS. Children with BWS should be screened at regular intervals (every 3 to 6 months) for renal, adrenal, and hepatic tumors. (author abst.) |
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