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Accession number;05A0361325
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| Title;Long-Surviving Patient With Isolated Absent Pulmonary Valve Syndrome: A Case Report |
| Author;
OKAJIMA KAZUE
(Izumi Munic. Hosp.)
KAWASE YOSHIO
(Izumi Munic. Hosp.)
HASEGAWA TAKAO
(Izumi Munic. Hosp.)
HATO KATSUNORI
(Izumi Munic. Hosp.)
NISHIMOTO MASAKI
(Izumi Munic. Hosp.)
YOSHIKAWA JUN'ICHI
(Graduate School of Medicine, Osaka City Univ., JPN)
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Journal Title;J Cardiol
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Journal Code:Y0264A
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ISSN:0914-5087
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VOL.45;NO.4;PAGE.165-171(2005)
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| Figure&Table&Reference;FIG.8, TBL.2, REF.15 |
| Pub. Country;Japan |
| Language;Japanese |
| Abstract;A 79-year-old woman was admitted for exertional dyspnea in September 2001. She had begun to experience unusual fatigue from the age of 40 years. Cardiac examination revealed a single S2, Levine grade II/VI presystolic murmur in the 5th left sternal border, and a right parasternal impulse. Echocardiography showed dilated right chambers and absence of pulmonary valve leaflets. Doppler echocardiography at the pulmonary annulus revealed a 'to and fro' pattern. Cardiac catheterization indicated the same diastolic pressures in the pulmonary artery and right ventricle. The diagnosis was absent pulmonary valve syndrome. Administration of a diuretic agent resulted in almost immediate improvement of symptoms. Absent pulmonary valve syndrome, generally associated with tetralogy of Fallot, often causes severe respiratory failure or right heart failure during infancy. A case of such long survival without associated cardiac anomalies is very rare. (author abst.) |
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